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Secondary Amenorrhea
Lisa L. Wil=
lett, MD
January 200=
8
Review Definitions
Primary Amenorrhea – normal secondary sexual
characteristics but no menarche by age 16, OR no secondary sexual
characteristics and no menarche by age 14.
Secondary Amenorrhea – absence of menses for 3 m=
onths
in women with previously normal menstruation, OR for 9 months in women with
previous oligomenorrhea.
Secondary amenorrhea is more common than primary. The four most common causes are: polycystic ovary syndrome (PCOS), =
hypothalamic
amenorrhea, ovarian failure, and hyperprolactinemia.
Case 1.
33 yoF
with abnormal menstrual cycles for 6 months. She has unpredictable times of her=
cycle
starting and stopping and for the past 3 months has not had a period. She wants to become pregnant and is
concerned. What is the approp=
riate
evaluation?
Obviously, first check a pregnancy test and then rule =
out
hypothyroidism and hyperprolactinemia.
Hypothyroidism:
usually, patients have clinical symptoms before amenorrhea develops,=
and
menstrual symptoms are usually hypermenorrhea o=
r oligomenorrhea, not amenorrhea.
Hyperprolactinemia:=
A level greater than 100 ng/mL suggests prolactinoma and an MRI should be done. If there is no adenoma, consider
medications (OCPs, antipsy=
chotics,
andtidepressants, antihype=
rtensives,
H2 blockers, opiates), although levels rarely exceed 100 ng/mL.
She has no sym=
ptoms of
hypothyroidism, no headaches or galactorrhea, a=
nd is
not on any medications. =
span>On exam, she has acne, facial hair, and
obesity. Her pelvic exam is normal. <=
/span>Her
TSH and prolactin levels are normal. What should you consider next?=
There are different ways to classify secondary
amenorrhea. One way is to con=
sider
where in the anatomy the defect is:
1. outflow tract obstruction
2. ovary=
3. pitui=
tary
4.
hypothalamus.
Some examples are below. (For exhaustive list, see Fertil Steril 2004;82(suppl 1):33-39)
|
Outflow obs=
truction
(Anatomic d=
efect)
(nl FSH)
|
Primary hypogonadism
(elevated F=
SH)
|
Pituitary
|
Hypothalami=
c
(low or nl FSH)
|
Other (endo=
crine)
|
|
1. Asherman’s
syndrome from
curettage or infection
2. cervical stenosis
3. obstructive fibroids or polyps
|
Premature ovarian failure
=
Automimmune
Chemotherapy
17-hyroxylase deficiency
Mumps
Pelvic irradiation
|
Prolactinoma
|
1. Anorexia, bulimia, excessive weight loss, stress,
exercise, nutrition related
2.CNS tumor or infection
3. Chronic illness:
cirrhosis, CKD, DM, IBD, severe
depression, immunodeficiency
|
1. Polycystic ovary syndrome
2. Androgen secreting tumor
3. Acromegaly
4. Cushings
5. Exogenous androgens
6. hyper or hypothyroidism
|
This patient h=
as signs
consistent with PCOS. =
o:p>
It is the most common cause of hy=
perandrogenic
chronic anovulation. The NIH criterion is chronic anovulation and hyperandrogenism=
,
with no other identified secondary cause.&=
nbsp;
The primary etiology is unknown, but resistance to insulin is
fundamental. Significantly el=
evated
testosterone or DHEA-S levels indicate a possible androgen-secreting tumor
(ovarian or adrenal). Patient=
s with
PCOS have excess unopposed circulating estrogen, increasing their risk of
endometrial cancer threefold. The
risk for diabetes is increased 2 to 5-fold.
Although there is some debate over the definition of P=
COS,
it is generally accepted that individuals must have 2 or 3 of the following=
:
- What is her be=
st
treatment option?
The primary treatment is weight loss through diet and
exercise. This can take month=
s, but
can lower androgen levels, improve hirsutism,
normalize menses, and decrease insulin resistence. Use of OCP or cyclic progestationa=
l
agents can maintain a normal endometrium (month=
ly 10
to 14 day regimens). Insulin
sensitizing agents like metfomin can reduce ins=
ulin resistance
and improve ovulation.
=
=

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